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Case Report
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J Mult Scler. 2010;1(1):27-29. Published online March 1, 2010.
- A Case of Neuromyelitis Optica Combined With Sjogren’s Syndrome Presenting Posterior Reversible Encephalopathy Syndrome
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Jaechun Hwang, Byoung Joon Kim, Kwang Ho Lee
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Department of Neurology, Sungkyunkwan University School of Medicine, Samsung Medical Center, Seoul, Korea
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- Abstract
- "Posterior reversible encephalopathy syndrome (PRES) is characterized by vasogenic subcortical edema, and its pathogenesis remains not well understood. Here we describe a patient of neuromyelitis optica (NMO) combined with Sjogren’s syndrome (SS) presenting PRES. The patient had relapsing-remitting optic neuritis and myelitis and acutely developed confusion and hemiparesis. Brain MRI revealed massive subcortical lesions. Autoantibodies and diagnostic tests satisfied the diagnostic criteria of SS. Anit-aquaporin-4 antibody was positive. Common water flux impairment may predispose NMO and SS to PRES. Journal of Multiple Sclerosis 1(1):27-29, 2010"
Keywords :PRES, Sjogren’s syndrome, Neuromyelitis optica