A Case of Neuromyelitis Optica Combined With Sjogren’s Syndrome Presenting Posterior Reversible Encephalopathy Syndrome |
Jaechun Hwang, Byoung Joon Kim, Kwang Ho Lee |
Department of Neurology, Sungkyunkwan University School of Medicine, Samsung Medical Center, Seoul, Korea |
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Abstract |
"Posterior reversible encephalopathy syndrome (PRES) is characterized by vasogenic subcortical edema, and its pathogenesis remains not well understood. Here we describe a patient of neuromyelitis optica (NMO) combined with Sjogren’s syndrome (SS) presenting PRES. The patient had relapsing-remitting optic neuritis and myelitis and acutely developed confusion and hemiparesis. Brain MRI revealed massive subcortical lesions. Autoantibodies and diagnostic tests satisfied the diagnostic criteria of SS. Anit-aquaporin-4 antibody was positive. Common water flux impairment may predispose NMO and SS to PRES. Journal of Multiple Sclerosis 1(1):27-29, 2010" |
Key Words:
PRES, Sjogren’s syndrome, Neuromyelitis optica |
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