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A Case of Neuromyelitis Optica Spectrum Disorder Presented with HyperCKemia and Dematomyositis-like Clinical Features

J Mult Scler > Volume 5(2); 2014 > Article
Journal of Multiple Sclerosis 2014;5(2):38-41.
Published online September 1, 2014.
고CK혈증, 피부근염 유사증상과 동반하여 발현한 시신경척수염범주질환 1예
석진명, 김주현, 조은빈, 조혜진, 김병준, 민주홍
성균관대학교 의과대학 신경과학교실, 삼성의료원 신경과
A Case of Neuromyelitis Optica Spectrum Disorder Presented with HyperCKemia and Dematomyositis-like Clinical Features
Jin Myoung Seok, Juhyeon Kim, Eun Bin Cho, Hye-Jin Cho, Byoung Joon Kim, Ju-Hong Min
Department of Neurology, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea
Abstract
"Neuromyelitis optica (NMO) is an autoimmune relapsing inflammatory disorder of the central nervous system. The detection of AQP4 antibody in NMO helped the recognition of various atypical clinicalpresentations including hyperCKemia. We report an anti-AQP4 antibody positive NMOSD patientpresented with hyperCKemia and dematomyositis-like clinical features. Journal of Multiple Sclerosis 5(2):38-41, 2014"
Key Words: Neuromyelitis optica, Neuromyelitis optica spectrum disorder, HyperCKemia, Aquaporin4, Dermatomyositis


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